argininosuccinicaciduria ar·gi·ni·no·suc·cin·ic·ac·i·du·ri·a (är'jə-nĭ-nō-sək-sĭn'ĭk-ās'ĭ-d&oobreve;r'ē-ə, -dy&oobreve;r'-, är'jə-nē'-)
n.
A disorder characterized by excessive excretion of argininosuccinic acid in the urine, epilepsy, ataxia, mental retardation, liver disease, and friable, tufted hair.