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inborn error of metabolism

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inborn error of metabolism

noun
any of a number of diseases in which an inherited defect (usually a missing or inadequate enzyme) results in an abnormality of metabolism 
WordNet® 3.0, © 2006 by Princeton University.
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Medical Dictionary

inborn error of metabolism n.
Any of a group of congenital disorders caused by an inherited defect in a single specific enzyme that results in a disruption or abnormality in a specific metabolic pathway.

The American Heritage® Stedman's Medical Dictionary
Copyright © 2002, 2001, 1995 by Houghton Mifflin Company. Published by Houghton Mifflin Company.
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